May 18, 2016 · Summary Summary. Evans syndrome is a very rare autoimmune disorder in which the immune system destroys the body's red blood cells, white blood cells and/or platelets. Affected people often experience thrombocytopenia (too few platelets) and Coombs' positive hemolytic anemia (premature destruction of red blood cells). This means that Evan's syndrome, or a subtype of Evan's syndrome, affects less than 200,000 people in the US population. Source - National Institutes of Health (NIH) Ophanet, a consortium of European partners, currently defines a condition rare when it affects 1 person per 2,000.Next: Symptoms of Evan's syndrome.
Evans Syndrome is a combination of two or more immune hematological disorders where your immune system attacks your white blood cells, red blood cells and/or platelets. These include immune thrombocytopenia (ITP), autoimmune hemolytic anemia (AIHA), and/or autoimmune neutropenia (AIN). These diagnoses might occur at the same time but can also occur in the same patient at two different . The Evans syndrome cohort had a mean age of 58.5 years at diagnosis, 51.2% were women, and 27.3% were classified as secondary Evans syndrome. The annual Evans syndrome incidence and prevalence rose significantly during the study period, to 1.8 per million person-years and 21.3 per million persons, respectively, in 2016.
The life expectancy of Evans Syndrome depend on each case. The remissions of the disease are common, as well as relapses. While some people with Evans syndrome may have a normal life expectancy, others have more recurrences and exarberaciones of the disease which can shorten the hope of lives and reduce the quality of life.